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Patient Stories

Restoring Sound, Reigniting Hope: A Girl's Journey With a Cochlear Implant

Hailey Pascarelli
Hailey Pascarelli

Eight-year-old Hailey Pascarelli is now adjusting to a new normal.

"Thank you for helping me be more confident about the surgery," said Pascarelli.

At her annual physical last year, doctors noticed Hailey was failing hearing tests in her right ear. That is when they determined she had completely lost her hearing on that side.

Referred to as Single-Sided Deafness, several tests were conducted to figure out the cause, but it still remains a mystery if it was a sudden loss of hearing or a condition that was developed overtime.

Hailey and her parents then met with Samantha Pepe, AuD, Pediatric Audiologist of Yale New Haven Children's Hospital (YNHCH), who decided Hailey would best served with a cochlear implant.

"Hailey is just a very positive person. She does everything with a smile on her face. She was nervous about the surgery - we all were - but like I said, she went in with a smile on her face. She makes it easy for us," said Amanda Porter, Hailey's mother.

An electronic device was surgically implanted under her skin behind her ear. On the outside, she was given a separate piece which includes a microphone, speech processor and transmitter.

The day Hailey received her device, there was something else planned. The author of her favorite book, "Daisy Doo - All The Sounds She Knew," surprised her with a FaceTime call. The author, Daisy Kent was a former contestant on the show, "The Bachelor." She also has a cochlear implant for hearing loss.

"It's refreshing to see that this gave her what she was expecting and what she wanted. It seems like we're already getting towards reaching her goal," said Samantha Pepe, AuD, YNHCH Pediatric Audiologist.

Watch a video about Hailey's journey.

Learn more about Pediatric Audiology at Yale New Haven Children's Hospital.

 

Pediatric hearing loss FAQ

How is hearing loss detected?

An audiologist will conduct a diagnostic hearing test as a first step. This test is more in-depth than a hearing screening and is performed slightly differently in most cases. Depending on the child’s age, there are several options to perform the diagnostic hearing test. A child can raise their hand when they hear the beep noise, conditioned play audiometry where the child plays a game in which they put the toy in the bucket if they hear a sound), visual reinforcement audiometry in which the child turns toward a stimulus played through speakers or headphones, or an Auditory Brainstem Response (ABR) test. An ABR is needed if the child cannot reliably inform the tester of their hearing levels in each ear. It is a typical testing measurement for infants or children who cannot test with headphones. ABR’s are done while the child is sleeping and involve the placement of electrodes on the head.

Are there other types of treatment options besides a cochlear implant?

For patients with single-sided deafness, other options would include a re-routing device such as a bone conduction device on a soft band or surgically implanted. Another option would be to go without hearing on one side and request special accommodation. Children with bilaterial hearing loss who are indicated for cochlear implantation should proceed with manual communication options such as American Sign Language (ASL) if a family is not interested in cochlear implants. Hearing aids can also be used for bilaterial patients as well.

Is hearing loss a genetic condition?

Some hearing losses are genetic. The diagnosis of a sensorineural hearing loss warrants a referral to genetics at the family doctor’s discretion to rule out genetic syndromes or recessive genetic hearing loss as a reason. It can also be caused by structural or anatomical abnormalities, congenital cytomegalovirus (CMV), exposure to ototoxic medications such as Cisplatin or meningitis. Another type of hearing loss is conductive hearing loss, which can be caused by ear infections, structural abnormalities, microtia or atresia or certain syndromes. Patients with conductive losses do not get cochlear implants and there are different options for them.

What are some warning signs of hearing loss?

Speech delay, inability to localize sound, not responding to environmental sounds, asking for frequent repetition, lack of attention or daydream in environments with significant background noise, often misunderstanding instructions or listening to the television at very high volumes.